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Table 2 Summary of JCS guidelines regarding the follow-up of patients with Kawasaki disease, starting at 1 year

From: Cardiovascular imaging in children and adults following Kawasaki disease

  Diagnostic testing Interval Invasive testing
No or transient CAAa Exercise ECG + echocardiogram Once, 5 years after disease b None
Small CAA (≤4 mm)a
 - Regressed (Exercise) ECG + echocardiogram Annual until age 7
Triennial until age 16
None
 - Persisting (Exercise) ECG + echocardiogram 3 months (until normalisation) None
 - Regressed or persisting In patients ≥ 10 years after onset, consider MDCT or MRCA at final evaluation.   
Medium CAA (>4 − <8 mm)a
 A. CAA > 4 − <6 mm
  - Regressed ECG + echocardiogram
X-ray + exercise ECG when necessary/feasible
MDCT or MRCA
Annual
5 years
Selective CAG on individual basis
  - Persisting ECG + echocardiogram
X-ray + exercise ECG when necessary/feasible
MDCT or MRCA
3–6 months
5 years
Selective CAG on individual basis
 B. CAA 6 − <8 mm
  - Regressed ECG + echocardiogram
X-ray + exercise ECG when necessary/feasible
MDCT or MRCA
Appropriate combination of techniques c
Annual
5 years
Invasive CAG once during convalescence and at time of disappearance of dilatation
  - Persisting ECG + echocardiogram
X-ray + exercise ECG when necessary/feasible
MDCT or MRCA
Appropriate combination of techniques c
3–6 months
5 years
Invasive CAG once during convalescence and at time of disappearance of dilatation
  Giant CAA (≥8 mm)a Tailor-made treatment with appropriate combination of (exercise) ECG, echocardiogram and other techniques c 3–6 months Invasive CAG during early convalescence phase
  1. From: Group JCSJW: Circ J 2014, 78(10):2521–25628
  2. MDCT Multidetector CT, MRCA MR Coronary Angiography
  3. aMeasured at 30 days after the onset of KD
  4. bAdditional follow-up from the second to fifth year and after the fifth year can be scheduled individually through consultation between patient and physician
  5. cImaging techniques include stress echocardiography, stress myocardial perfusion scintigraphy, invasive coronary angiography (CAG), Intravenous Ultrasound, Cardiac Magnetic Resonance Imaging, Magnetic Resonance Angiography and Multidetector CT