Fig. 13

Imaging in neurofibromatosis (NF-1). a Plexiform neurofibromatosis in a 36-year-old woman with NF-1. Axial contrast enhanced image from upper abdomen shows a large lobulated hypodense mass (arrow) encasing the vessels without causing any narrowing. The adjacent organs are displaced by the central mass without invasion. b Plexiform neurofibromatosis and pheochromocytoma in a 45-year-old man with NF-1. Contrast enhanced CT scan shows an ill-defined hypodense plexiform neurofibromatosis mass (arrow) extending along the portal triad in the liver. The heterogeneously enhancing right adrenal mass (arrowhead) was a pheochromocytoma on resection. c, d A 29-year-old man with NF-1. Multiple low density well-defined hypodense neurofibromas along the sacral plexus were seen in the pelvis on both sides (arrows) on CT scan (c). On a follow up CT scan (d), a large new heterogeneous solid mass (arrow) was seen in left retroperitnoeum, proven to be a malignant peripheral nerve sheath tumour on resection. A neurofibroma is also seen in the right chest (arrow)