Fig. 23

Closed encephalocele in MPS VI. Closed encephalocele in patient affected by MPS VI (same patient as in Fig. 12). Coronal MDCT image of middle cranial fossa (a), obtained at the level of the pterygoid processes, revealing a bone depression of the right great wing of the sphenoid. The corresponding coronal T2-weighted MRI image (b) demonstrates the pouch filled with cerebrospinal fluid and brain parenchyma