Fig. 19
From: Imaging findings of mucopolysaccharidoses: a pictorial review
Involvement of the craniocervical junction: recurrence after surgery. Craniocervical junction appearance in an MPS VI patient before (a) and after (a”) the decompressive surgical procedure: note the improvement in size of the craniocervical junction, with enlargement of subarachnoid spaces after the surgical procedure. b and b” show recurrence of stenosis of the craniocervical junction in an MPS IV patient 3 and 12 years respectively after surgery; the recurrence is due to progression of GAG accumulation