Fig. 18
From: Imaging findings of mucopolysaccharidoses: a pictorial review
Involvement of the craniocervical junction. Sagittal T2-weighted fast spin-echo MRI acquisitions at the craniocervical junction in a patient affected by MPS VI before (a) and after (c) the decompressive surgical procedure. Magnifications (b and d) show a T2 hypointense lesion surrounding the odontoid process (white arrowhead, b) with marked narrowing of the foramen magnum and cord compression; the stenosis improved moderately after surgery. Note also the abnormal J-shaped sella (white arrow, d)