Fig. 11

Dysostosis multiplex of long bones. Dysostosis multiplex of hands and wrists in a 5-year-old boy (b) and in a 15-year-old female (d), both affected by MPS VI (radiographs are compared with normal hands and wrists belonging to subjects of the same age, respectively a and c). The main imaging findings encountered in these areas are reported: the V-shaped hypoplastic distal ulna and radius (white arrow), the presence of small irregular carpal bones (curved white arrow), the broad and proximally pointed short metacarpals (white arrowhead) and the bullet-shaped phalanges (empty white arrow)