Fig. 10

Severe LPAC syndrome with secondary intrahepatic cholangiocarcinoma formation in a 55-year-old woman. Maximum intensity projection coronal MRCP (a), and transverse T2-weighted acquisition show right biliary irregularities and dilated left bile ducts filled with several small intrahepatic stones (white arrow in b). Two years later, T1-weighted transverse acquisitions with fat saturation after gadolinium chelate injection obtained at portal phase (c) and transverse T2-weighted acquisition (d) show an intrahepatic large mass with irregular contrast enhancement (white star). Liver biopsy confirmed the diagnosis of intrahepatic cholangiocarcioma