Variable | Serum ferritin ≤ 2500 ug/L (n = 33) | Serum ferritin > 2500 ug/L (n = 33) | p value |
---|---|---|---|
Age (years); mean ± SD | 14.78 ± 6.85 | 16.55 ± 7.18 | 0.315 |
Males; n (%) | 15 (46.9) | 19 (57.6) | 0.388 |
Iron Overload (mg/kg/day); mean ± SD | 0.17 ± 0.14 | 0.28 ± 0.13 | 0.001 |
On chelation; n (%) | 20 (62.5) | 32 (97.0) | 0.001 |
Poor compliance to chelation; n (%) | 6 (31.6) | 15 (50.0) | 0.204 |
Pre-transfusion hemoglobin (g/dL); mean ± SD | 7.66 ± 1.46 | 8.37 ± 1.30 | 0.046 |
HbS (%); mean ± SD | 63.28 ± 16.04 | 59.57 ± 24.29 | 0.504 |
HbF (%); median (IQR) | 6.2 (0.8–12.2) | 3.6 (1.3–10) | 0.579 |
Lactate dehydrogenase (IU/L); mean ± SD | 547.38 ± 331.71 | 525.21 ± 204.67 | 0.749 |
Total bilirubin (mg/dL); mean ± SD | 2.59 ± 1.50 | 2.60 ± 1.09 | 0.970 |
Indirect bilirubin (mg/dL) | 1.33 (0.9–2.18) | 1.8 (0.9–2.12) | 0.549 |
Serum amylase; mean ± SD | 57.41 ± 24.46 | 56.12 ± 18.74 | 0.815 |
LIC (mg/g liver dry weight); median (IQR) | 6.19 (3.06–11.02) | 16.16 (12.94–24.7) | 0.000 |
Normal; n (%) | 7 (21.9) | 0 (0.0) | 0.000 |
Mild; n (%) | 13 (40.6) | 2 (6.1) | |
Moderate; n (%) | 10 (31.3) | 14 (42.4) | |
Severe; n (%) | 2 (6.3) | 17 (51.5) | |
Cardiac T2* (msec); mean ± SD | 32.03 ± 5.09 | 30.79 ± 7.80 | 0.454 |
Pancreatic MRI (msec); median (IQR) | 52.85 (35.35 – 83.5) | 54.9 (31.8 – 87) | 0.847 |