Study site | N | Age (range, median) | Ankles Imaged | Elbows imaged | Knees imaged | Hemophilia type | Baseline FVIII/IX Level* (%) | Pettersson score | HJHS score (range, median) |
---|---|---|---|---|---|---|---|---|---|
1 | 22 | 7–17, 13 | 8 | 7 | 7 | A:N = 17 | 0:N = 13; | Score 0:N = 1 | 7–15, 9 |
1: N = 4 | Scores 1–3:N = 8 | ||||||||
Scores 4–7:N = 5 | |||||||||
B:N = 5 | 0:N = 4 | Scores ≥ 8:N = 8 | |||||||
1:N = 1 | |||||||||
2 | 12 | 8–18, 11.5 | 4 | 4 | 4 | A:N = 12 | 0:N = 5 | Score 0:N = 0 | 3–16, 11.5 |
1:N = 7 | Scores 1–3:N = 4 | ||||||||
Scores 4–7:N = 4 | |||||||||
Scores ≥ 8:N = 4 | |||||||||
3 | 29 | 5–17, 13 | 21 | 0 | 8 | A:N = 23 | 0:N = 20 | Score 0:N = 14 | 0–16, 4.5 |
1:N = 3 | Scores 1–3:N = 4 | ||||||||
B:N = 3 | 0:N = 2 | Scores 4–7:N = 5 | |||||||
1:N = 1 | Scores ≥ 8:N = 6 | ||||||||
vWD type 3:N = 3** |